Cervicothoracic fibrous dysplasia

Abstract

Polyostotic Fibrous Dysplasia (PFD) is a form of fibrous displasia affecting more than one bone, mainly craniofacial, ribs and costal, femoral, pelvic and tibial bones. In less proportion it also can develope in the vertebral column. Due to it’s pathophysiologic characteristic, it can compromise any bone. We present the case of a 25 years old, female patient, with a history of moderate shooting pain over the right scapula, with proximal weakness of the right lower extremity followed by weakness of contralateral extremity, abdominal paresthesia and lose of sphincters’ control. Due to the image studies findings (thoracic X-ray, cervico-dorsal computed tomography and magnetic resonance imaging), the subject was submitted to a medullary decompression with dorsal approach. Histopathologic results, from the tissue sample taken during surgery, confirmed the presence of bone fibrous dysplasia. Following the detection of PFD lesions, it is paramount to make imaging studies to the vertebral column for immediate detection of lesions in this site, and bring timely treatment to maintain a stable column and hamper neurologic damage.